Altered germinal center reaction and abnormal B cell peripheral maturation in PI3KR1-mutated patients presenting with HIGM-like phenotype
Articolo
Data di Pubblicazione:
2015
Tipologia CRIS:
1.1 Articolo in rivista
Keywords:
B cells; Germinal Center (GC) reaction; Hyper-IgM syndrome; PIK3R1; B-Lymphocytes; Child, Preschool; Female; Germinal Center; Humans; Hyper-IgM Immunodeficiency Syndrome; Infant; Male; Mutation; Phenotype; Phosphatidylinositol 3-Kinases; RNA Splice Sites; Sequence Analysis, DNA; Immunology; Immunology and Allergy
Elenco autori:
Lougaris, Vassilios; Faletra, Flavio; Lanzi, Gaetana; Vozzi, Diego; Marcuzzi, Annalisa; Valencic, Erica; Piscianz, Elisa; Bianco, Annamonica; Girardelli, Martina; Baronio, Manuela; Loganes, Claudia; Fasth, Anders; Salvini, Filippo; Trizzino, Antonino; Moratto, Daniele; Facchetti, Fabio; Giliani, Silvia Clara; Plebani, Alessandro; Tommasini, Alberto
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