Data di Pubblicazione:
2016
Abstract:
Autoinflammatory diseases cause systemic inflammation that can result in damage to multiple organs. A validated instrument is essential to quantify damage in individual patients and to compare disease outcomes in clinical studies. Currently, there is no such tool. Our objective was to develop a common autoinflammatory disease damage index (ADDI) for familial Mediterranean fever, cryopyrin-associated periodic syndromes, tumour necrosis factor receptor-associated periodic fever syndrome and mevalonate kinase deficiency.
Tipologia CRIS:
1.1 Articolo in rivista
Keywords:
Familial Mediterranean Fever; Fever Syndromes; Outcomes research; Patient perspective
Elenco autori:
Ter Haar, Nienke M; Annink, Kim V; Al Mayouf, Sulaiman M; Amaryan, Gayane; Anton, Jordi; Barron, Karyl S; Benseler, Susanne M; Brogan, Paul A; Cantarini, Luca; Cattalini, Marco; Cochino, Alexis Virgil; De Benedetti, Fabrizio; Dedeoglu, Fatma; De Jesus, Adriana A; Della Casa Alberighi, Ornella; Demirkaya, Erkan; Dolezalova, Pavla; Durrant, Karen L; Fabio, Giovanna; Gallizzi, Romina; Goldbach Mansky, Raphaela; Hachulla, Eric; Hentgen, Veronique; Herlin, Troels; Hofer, Michaël; Hoffman, Hal M; Insalaco, Antonella; Jansson, Annette F; Kallinich, Tilmann; Koné Paut, Isabelle; Kozlova, Anna; Kuemmerle Deschner, Jasmin B; Lachmann, Helen J; Laxer, Ronald M; Martini, Alberto; Nielsen, Susan; Nikishina, Irina; Ombrello, Amanda K; Ozen, Seza; Papadopoulou Alataki, Efimia; Quartier, Pierre; Rigante, Donato; Russo, Ricardo; Simon, Anna; Trachana, Maria; Uziel, Yosef; Ravelli, Angelo; Gattorno, Marco; Frenkel, Joost
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